Congenital pulmonary airway malformation (Phenotype)

Synonyms:HP:0006540, HP:0006545, CCAM, Congenital cystic adenomatoid malformation of the lung, Congenital cystic disease of the lung, Cystic adenomatoid lung disease

Id:HP:0010959

Description:Congenital pulmonary airway malformation (CPAM) - previously known as congenital cystic adenomatoid malformation (CCAM) - is a relatively rare developmental malformation of the lower respiratory tract. It is a hamartomatous, dysplastic developmental abnormality of the lung characterized by abnormal airway patterning during lung branching morphogenesis and is formed by abnormal branching of the immature bronchioles.

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	Label	Description
	PT 96AAYCKG Subject (Entity type)	A subject from Kids First produced as part of the SD PREASA7S project
	PT N35R1FCW Subject (Entity type)	A subject from Kids First produced as part of the SD PREASA7S project
	PT TV41VP87 Subject (Entity type)	A subject from Kids First produced as part of the SD PREASA7S project
	PT TNNCNGE9 Subject (Entity type)	A subject from Kids First produced as part of the SD PREASA7S project
	PT X3NQGNNR Subject (Entity type)	A subject from Kids First produced as part of the SD PREASA7S project
	PT 2Q53BXVY Subject (Entity type)	A subject from Kids First produced as part of the SD PREASA7S project
	PT Z2KQD4XB Subject (Entity type)	A subject from Kids First produced as part of the SD PREASA7S project
	PT VV2SM600 Subject (Entity type)	A subject from Kids First produced as part of the SD PREASA7S project
	PT 4PFP2MHD Subject (Entity type)	A subject from Kids First produced as part of the SD PREASA7S project
	PT 5SFFE2ZV Subject (Entity type)	A subject from Kids First produced as part of the SD PREASA7S project